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Dernières publications
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Valentina Taglietti, Kaouthar Kefi, Lea Rivera, Oriane Bergiers, Nastasia Cardone, et al.. Thyroid-stimulating hormone receptor signaling restores skeletal muscle stem cell regeneration in rats with muscular dystrophy. Science Translational Medicine, 2023, 15 (685), ⟨10.1126/scitranslmed.add5275⟩. ⟨hal-04150315⟩
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A. Morin, Amalia Stantzou, Olga N. Petrova, John C.W. Hildyard, T. Tensorer, et al.. Dystrophin myonuclear domain restoration governs treatment efficacy in dystrophic muscle. Proceedings of the National Academy of Sciences of the United States of America, 2023, 120 (2), ⟨10.1073/pnas.2206324120⟩. ⟨hal-04122777⟩
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Valentina Taglietti, Kaouthar Kefi, Iwona Bronisz-Budzyńska, Busra Mirciloglu, Mathilde Rodrigues, et al.. Duchenne muscular dystrophy trajectory in R-DMDdel52 preclinical rat model identifies COMP as biomarker of fibrosis. Acta Neuropathologica Communications, 2022, 10 (1), ⟨10.1186/s40478-022-01355-2⟩. ⟨hal-03828280⟩
Chiffres clés
48
Publications avec texte intégral
Open Access
67 %
Mots clés
Calcium
CaV subunits
Skeletal muscle
Cardiomyopathy
Human Umbilical Vein Endothelial Cells
Gene Expression Regulation/drug effects
Cell homeostasis
Muscle Strength
Gene expression
Animals
CTNNB1
NNOS
Duchenne muscular dystrophy DMD
Hear
Inhibitors
Long QT
Diseases
Dystrophin-EGFP
Invivo
Myotendinous junction
Inbred C57BL
Humans
BMD
Becker muscular dystrophy BMD
Modificateurs de gènes
Becker muscular dystrophy
Metabolism
Molecular Sequence Data
Male
Delivery
Base Sequence
Dystrophie musculaire de Becker
DMO
Gene modifiers
Liver
Muscles/physiopathology
MiARN
Activin Receptors
Energy Metabolism/drug effects
Ex-vivo
Multiresolution modeling
Centronuclear myopathy
MES
Hepatocellular carcinoma
Mdx mouse
Drp1
Allele‐specific silencing therapy
Homeostasis
Myogenesis
DMD
Duchenne muscular dystrophy
Becker BMD muscular dystrophy
Autophagy
Knockout
Muscular dystrophy
Morphogenesis
Immunoglobulin Fc Fragments/pharmacology
Dystrophie Musculaire de Becker BMD
Cardiomyopathie
Dystrophie Musculaire de Duchenne DMD
LncARN
Multi resolution modeling
Animal/physiopathology
Muscle
Cultured
Dystrophy
Epigenetics
Dystrophine
Long noncoding RNA
Mice
Inbred mdx
Muscle Biology
Mitochondrial fission
Cachexia
Molecular docking
CaVβs
Cell Line
LKB1
Cell Biology
Cells
Duchenne DMD dystrophy
Dynamin 2
Clinical trials
LncRNA
DHPR α1S
Génomique
Muscular Atrophy
Dystrophin
Antisense oligonucleotides
L-Type
Exon skipping
Genomic
Muscular Dystrophy
Becker muscular dystrophy BMD Duchenne muscular dystrophy DMD miRNA nNOS
Calcium Channels
Multi exon skipping
CD38
Muscle development
Dystrophin central domain
NAD+